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GAA Recombinant Rabbit mAb (bsm-62357R)  
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產(chǎn)品編號(hào) bsm-62357R
英文名稱 GAA Recombinant Rabbit mAb
中文名稱 α葡萄糖苷酶/溶酶體α-葡糖苷酶重組兔單抗
別    名 Acid maltase; GAA; Glucosidase alpha acid; LYAG.  
抗體來(lái)源 Rabbit
克隆類型 Recombinant
克 隆 號(hào) 3H15
交叉反應(yīng) Human,Mouse,Rat
產(chǎn)品應(yīng)用 WB=1:500-1000
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
理論分子量 105 kDa
檢測(cè)分子量 120,100,75
性    狀 Liquid
濃    度 1mg/ml
免 疫 原 A synthesized peptide derived from human Lysosomal alpha glucosidase: 140-210 
亞    型 IgG
純化方法 affinity purified by Protein A
緩 沖 液 10mM phosphate buffered saline(pH 7.4) with 150mM sodium chloride, 0.05% BSA, 0.02% Proclin300 and 50% glycerol.
保存條件 Store at 4℃ for short term. Store at -20℃ for long term. Avoid repeated freeze/thaw cycles.
注意事項(xiàng) This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
PubMed PubMed
產(chǎn)品介紹 Essential for the degradation of glycogen in lysosomes. Has highest activity on alpha-1,4-linked glycosidic linkages, but can also hydrolyze alpha-1,6-linked glucans.

SWISS:
P10253

Gene ID:
2548

產(chǎn)品圖片
Western blot analysis of Human fetal liver lysate. Using GAA (bsm-62357R) monoclonal antibody at 1:1000 dilution and 4°C overnight incubation. Followed by conjugated secondary antibody incubation at r.t. for 60 min.
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